Congenitally corrected transposition of the great arteries (CCTGA) is a rare heart defect. Only 0.5 to 1 percent of all people with heart defects have CCTGA. This means there are about 5,000 to 10,000 people in the United States with this condition.
What is a baffle in cardiac surgery?
A baffle is a surgically-created tunnel or wall within the heart or major blood vessels used to redirect the flow of blood. They are used in some types of heart abnormalities that a child is born with known as congenital heart defects.
What is L-TGA?
Levo- or L-looped transposition of the great arteries (L-TGA) is a rare form of congenital heart disease characterized by atrioventricular (AV) and ventriculoarterial discordance (figure 1). It is also commonly referred to as congenitally corrected TGA, double discordance, or ventricular inversion.
What is CCTGA?
Congenitally corrected transposition of the great arteries (CCTGA) is a rare heart defect in which the heart’s lower half is reversed. It is also called L-TGA. It is different from and much less common than “regular” transposition of the great arteries (TGA or D-TGA).
Is Cctga hereditary?
In conclusion, CCTGA is not always sporadic in families. The pattern of inheritance, the presence of consanguinity among parents and the recurrence of situs inversus could suggest, in some families, an autosomal recessive mechanism with similarities with that occurring in some pedigrees with heterotaxia.
How many people in the world have Cctga?
Congenitally corrected transposition of the great vessels (CCTGA; l-TGA) is an uncommon congenital heart abnormality, occurring in 0.5% of the population.
What is baffle obstruction?
Baffle Obstruction: The baffles, that were created to switch the blood flow in the heart, are usually made from a synthetic material, called GorTex. With time, the baffles can scar which causes difficulty with blood flow (obstruction) in the heart.
What is the mustard heart procedure?
The Mustard Procedure allows total correction of transposition of the great vessels. The procedure employs a baffle to redirect caval blood flow to the left atrium which then pumps blood to the left ventricle which then pumps the deoxygenated blood to the lungs.
What is Levo transposition?
Levo-Transposition of the great arteries is an acyanotic congenital heart defect in which the primary arteries (the aorta and the pulmonary artery) are transposed, with the aorta anterior and to the left of the pulmonary artery; the morphological left and right ventricles with their corresponding atrioventricular …
What is BT shunt surgery?
A Blalock-Taussig (BT) shunt is a small tube that connects the arterial circulation to the pulmonary circulation in order to get more blood to the lungs. This is the first in a series of operations required to correct complex congenital (present at birth) heart defects.
What is Hlhs?
Hypoplastic left heart syndrome (HLHS) is a birth defect that affects normal blood flow through the heart. As the baby develops during pregnancy, the left side of the heart does not form correctly. Hypoplastic left heart syndrome is one type of congenital heart defect. Congenital means present at birth.
What is ventricular inversion?
Definition. Ventricular inversion refers to a specific congenital heart defect in which the ventricles are exchanged in position so that the left atrium enters the right ventricle and the right atrium enters the left ventricle.
What is the double switch procedure?
The double switch procedure is a surgical technique used to repair congenitally corrected transposition of the great arteries (L-TGA), which is a cardiovascular anomaly with atrioventricular and ventriculoarterial discordance.
What is the double switch procedure for congenitally corrected transposition?
The double switch procedure for anatomical repair of congenitally corrected transposition of the great arteries in infants and children. European heart journal. 18 (9): 1470-7. Pubmed
What is the double switch procedure for l-TGA?
The double switch procedure is usually performed in L-TGA patients of several months to years of age. The aim is to minimize or prevent right ventricular or tricuspid valve dysfunction that complicates the anomaly. Prior to correction, patients may require training of the morphologic left ventricle using pulmonary artery banding.
